Terminology Service for NFDI4Health
arrhythmogenic right ventricular cardiomyopathy
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http://purl.obolibrary.org/obo/MONDO_0016587
Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a heart muscle disease that consists in progressive dystrophy of primarily the right ventricular myocardium with fibro-fatty replacement and ventricular dilation, and that is clinically characterized by ventricular arrhythmias and a risk of sudden cardiac death. [ ]
Term info
Label
arrhythmogenic right ventricular cardiomyopathy
Synonyms
- ARVC
- ARVC cardiomyopathy
- ARVD
- arrhythmogenic RVD
- arrhythmogenic right ventricular cardiomyopathy
- arrhythmogenic right ventricular dysplasia
- arrhythmogenic right ventricular dysplasia/cardiomyopathy
- right ventricular dysplasia
Subsets
gard_rare, disease_grouping, clingen, ordo_group_of_disorders
closeMatch
http://identifiers.org/meddra/10058093
exactMatch
http://linkedlifedata.com/resource/umls/id/CN221565, http://linkedlifedata.com/resource/umls/id/C0349788, http://purl.obolibrary.org/obo/NCIT_C84571, http://identifiers.org/snomedct/281170005, http://purl.obolibrary.org/obo/Orphanet_247, http://purl.obolibrary.org/obo/DOID_0050431, http://identifiers.org/mesh/D019571, http://linkedlifedata.com/resource/umls/id/CN239850
id
MONDO:0016587
narrowMatch
https://icd.codes/icd10cm/I42.8