Terminology Service for NFDI4Health

frontotemporal dementia

Go to external page http://purl.obolibrary.org/obo/MONDO_0017276


Frontotemporal dementia (FTD) comprises a group of neurodegenerative disorders, characterized by progressive changes in behavior, executive dysfunction and language impairment, as a result of degeneration of the medial prefrontal and frontoinsular cortices. Four clinical subtypes have been identified: semantic dementia, progressive non-fluent aphasia, behavioral variant FTD and right temporal lobar atrophy. [ ]

Term info

Label

frontotemporal dementia

Synonyms
  • FTD
  • Wilhemsen-Lynch disease
  • frontotemporal lobar degeneration
  • multiple system tauopathy with presenile dementia
  • pallidopontonigral degeneration
database cross reference
Subsets

disease_grouping, ordo_group_of_disorders

closeMatch

http://identifiers.org/meddra/10068968

exactMatch

http://purl.obolibrary.org/obo/NCIT_C84719, http://identifiers.org/mesh/D057180, http://linkedlifedata.com/resource/umls/id/C0338451, http://purl.obolibrary.org/obo/Orphanet_282, http://linkedlifedata.com/resource/umls/id/C0520716, http://purl.obolibrary.org/obo/DOID_9255

excluded subClassOf

http://purl.obolibrary.org/obo/MONDO_0003996

has related synonym

frontotemporal lobe dementia (FLDEM), MSTD

id

MONDO:0017276

narrowMatch

https://icd.codes/icd10cm/G31.0