Terminology Service for NFDI4Health

dysembryoplastic neuroepithelial tumor

Go to external page http://www.ebi.ac.uk/efo/EFO_0005551


A benign glial-neuronal neoplasm. It is usually supratentorial, located, generally, in the cortex and occurs in children and young adults with a long-standing history of partial seizures. A histologic hallmark of this tumor is the 'specific glioneuronal element', characterized by columns, made up of bundles of axons, oriented perpendicularly to the cortical surface.B [ ]

Term info

Label

dysembryoplastic neuroepithelial tumor

Synonyms
  • DNET
  • DNT
  • dysembryoplastic neuroepithelial neoplasm
  • dysembryoplastic neuroepithelial tumor
  • dysembryoplastic neuroepithelial tumor (morphologic abnormality)
database cross reference
Subsets

gard_rare, ordo_disease

closeMatch

http://identifiers.org/snomedct/128788005

exactMatch

http://identifiers.org/snomedct/87211000119104, http://purl.obolibrary.org/obo/DOID_2679, http://linkedlifedata.com/resource/umls/id/C1266177, http://purl.obolibrary.org/obo/NCIT_C9505, http://purl.obolibrary.org/obo/Orphanet_251946

id

EFO:0005551

see also

https://rarediseases.info.nih.gov/diseases/10640/dysembryoplastic-neuroepithelial-tumor