Terminology Service for NFDI4Health

Primary progressive aphasia

Go to external page http://www.ebi.ac.uk/efo/EFO_0009053


Primary progressive aphasia (PPA) is a neurodegenerative disorder, characterized by a primary dissolution of language, with relative sparing of other mental faculties for at least the first 2 years of illness. PPA is recognized as the language variant in the frontotemporal dementia (FTD) spectrum of disorders. PPA can be classified into 3 subtypes based on specific speech and language features: semantic dementia (SD), progressive non-fluent aphasia (PNFA) and logopenic progressive aphasia (lv-PPA). [ ]

Term info

Label

Primary progressive aphasia

Synonyms
  • Mesulam syndrome
  • PPA
  • primary progressive aphasia
database cross reference
Subsets

disease_grouping, ordo_group_of_disorders

exactMatch

http://identifiers.org/mesh/D018888, http://purl.obolibrary.org/obo/Orphanet_95432, http://linkedlifedata.com/resource/umls/id/C0282513, http://purl.obolibrary.org/obo/NCIT_C85024

has related synonym

primary progressive aphasia syndrome

id

EFO:0009053

narrowMatch

https://icd.codes/icd10cm/G31.0

term editor

Hannah McLaren

Term relations