Terminology Service for NFDI4Health
A subacute or chronic inflammatory disease of muscle and skin, marked by proximal muscle weakness and a characteristic skin rash. The illness occurs with approximately equal frequency in children and adults. The skin lesions usually take the form of a purplish rash (or less often an exfoliative dermatitis) involving the nose, cheeks, forehead, upper trunk, and arms. The disease is associated with a complement mediated intramuscular microangiopathy, leading to loss of capillaries, muscle ischemia, muscle-fiber necrosis, and perifascicular atrophy. The childhood form of this disease tends to evolve into a systemic vasculitis. Dermatomyositis may occur in association with malignant neoplasms. (From Adams et al., Principles of Neurology, 6th ed, pp1405-6)
Instance info
Synonyms
Polymyositis-Dermatomyositis, Juvenile Dermatomyositis (DE), Dermatomyositis, bei Kindern (DE), Myositis, Juvenile, Dermatomyositis, Juvenile, Dermatomyositis (DE), Dermatopolymyositis (DE), Juvenile Myositis, Juvenile Dermatomyositis, Dermatomyositis, Childhood Type, Dermatopolymyositis, Dermatomyositis, bei Erwachsenen (DE), Dermatomyositis-Polymyositis (DE), Polymyositis Dermatomyositis, Dermatomyositis, Adult Type, Adult Type Dermatomyositis, Childhood Type Dermatomyositis
AN
coordinate with PARANEOPLASTIC SYNDROMES if pertinent
AQL
BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI
DC
1
DX
19660101
MDA
19990101
MMR
20180521
MN
C17.800.185,C10.668.491.562.575.500,C17.300.250,C05.651.594.819.500
QB
http://purl.bioontology.org/ontology/MESH/Q000097,http://purl.bioontology.org/ontology/MESH/Q000175,http://purl.bioontology.org/ontology/MESH/Q000196,http://purl.bioontology.org/ontology/MESH/Q000151,http://purl.bioontology.org/ontology/MESH/Q000150,http://purl.bioontology.org/ontology/MESH/Q000191,http://purl.bioontology.org/ontology/MESH/Q000139,http://purl.bioontology.org/ontology/MESH/Q000534,http://purl.bioontology.org/ontology/MESH/Q000378,http://purl.bioontology.org/ontology/MESH/Q000532,http://purl.bioontology.org/ontology/MESH/Q000235,http://purl.bioontology.org/ontology/MESH/Q000652,http://purl.bioontology.org/ontology/MESH/Q000453,http://purl.bioontology.org/ontology/MESH/Q000178,http://purl.bioontology.org/ontology/MESH/Q000134,http://purl.bioontology.org/ontology/MESH/Q000276,http://purl.bioontology.org/ontology/MESH/Q000473,http://purl.bioontology.org/ontology/MESH/Q000000981,http://purl.bioontology.org/ontology/MESH/Q000451,http://purl.bioontology.org/ontology/MESH/Q000517,http://purl.bioontology.org/ontology/MESH/Q000382,http://purl.bioontology.org/ontology/MESH/Q000469,http://purl.bioontology.org/ontology/MESH/Q000601,http://purl.bioontology.org/ontology/MESH/Q000821,http://purl.bioontology.org/ontology/MESH/Q000523,http://purl.bioontology.org/ontology/MESH/Q000401,http://purl.bioontology.org/ontology/MESH/Q000201,http://purl.bioontology.org/ontology/MESH/Q000662,http://purl.bioontology.org/ontology/MESH/Q000266,http://purl.bioontology.org/ontology/MESH/Q000145,http://purl.bioontology.org/ontology/MESH/Q000188,http://purl.bioontology.org/ontology/MESH/Q000628,http://purl.bioontology.org/ontology/MESH/Q000209,http://purl.bioontology.org/ontology/MESH/Q000208,http://purl.bioontology.org/ontology/MESH/Q000503
SIB
http://purl.bioontology.org/ontology/MESH/D009372,http://purl.bioontology.org/ontology/MESH/D011537,http://purl.bioontology.org/ontology/MESH/D012868,http://purl.bioontology.org/ontology/MESH/D012625,http://purl.bioontology.org/ontology/MESH/D011536,http://purl.bioontology.org/ontology/MESH/D000796,http://purl.bioontology.org/ontology/MESH/D017486,http://purl.bioontology.org/ontology/MESH/D017441,http://purl.bioontology.org/ontology/MESH/D012393,http://purl.bioontology.org/ontology/MESH/D057088,http://purl.bioontology.org/ontology/MESH/D007868,http://purl.bioontology.org/ontology/MESH/D012872,http://purl.bioontology.org/ontology/MESH/D014972,http://purl.bioontology.org/ontology/MESH/D012874,http://purl.bioontology.org/ontology/MESH/D012873,http://purl.bioontology.org/ontology/MESH/D017445,http://purl.bioontology.org/ontology/MESH/D012592,http://purl.bioontology.org/ontology/MESH/D012595,http://purl.bioontology.org/ontology/MESH/D017444,http://purl.bioontology.org/ontology/MESH/D017520,http://purl.bioontology.org/ontology/MESH/D012594,http://purl.bioontology.org/ontology/MESH/D017443,http://purl.bioontology.org/ontology/MESH/D010411,http://purl.bioontology.org/ontology/MESH/D012875,http://purl.bioontology.org/ontology/MESH/D012878,http://purl.bioontology.org/ontology/MESH/D000071380,http://purl.bioontology.org/ontology/MESH/D055535,http://purl.bioontology.org/ontology/MESH/D010859,http://purl.bioontology.org/ontology/MESH/D004387,http://purl.bioontology.org/ontology/MESH/D006201,http://purl.bioontology.org/ontology/MESH/D009634,http://purl.bioontology.org/ontology/MESH/D008947,http://purl.bioontology.org/ontology/MESH/D012883,http://purl.bioontology.org/ontology/MESH/D010023,http://purl.bioontology.org/ontology/MESH/D008382,http://purl.bioontology.org/ontology/MESH/D015434,http://purl.bioontology.org/ontology/MESH/D008068,http://purl.bioontology.org/ontology/MESH/D017577,http://purl.bioontology.org/ontology/MESH/D005076,http://purl.bioontology.org/ontology/MESH/D058568,http://purl.bioontology.org/ontology/MESH/D002481,http://purl.bioontology.org/ontology/MESH/D065134,http://purl.bioontology.org/ontology/MESH/D003095,http://purl.bioontology.org/ontology/MESH/D008180,http://purl.bioontology.org/ontology/MESH/D010787,http://purl.bioontology.org/ontology/MESH/D011711,http://purl.bioontology.org/ontology/MESH/D002357,http://purl.bioontology.org/ontology/MESH/D007642,http://purl.bioontology.org/ontology/MESH/D008415,http://purl.bioontology.org/ontology/MESH/D005148,http://purl.bioontology.org/ontology/MESH/D006712,http://purl.bioontology.org/ontology/MESH/D001941,http://purl.bioontology.org/ontology/MESH/D013543,http://purl.bioontology.org/ontology/MESH/D008178,http://purl.bioontology.org/ontology/MESH/D011561,http://purl.bioontology.org/ontology/MESH/D003483,http://purl.bioontology.org/ontology/MESH/D004890,http://purl.bioontology.org/ontology/MESH/D009260,http://purl.bioontology.org/ontology/MESH/D012216,http://purl.bioontology.org/ontology/MESH/D000074079,http://purl.bioontology.org/ontology/MESH/D012536,http://purl.bioontology.org/ontology/MESH/D054989,http://purl.bioontology.org/ontology/MESH/D056846,http://purl.bioontology.org/ontology/MESH/D003872,http://purl.bioontology.org/ontology/MESH/D005534,http://purl.bioontology.org/ontology/MESH/D007636,http://purl.bioontology.org/ontology/MESH/D006229
TERMUI
T372461,T372463,T372462,T372464,T011553,T000922806,T000922805
TH
NLM (2018),ORD (2010),NLM (1966),NLM (2000)
cui
C0263666,C0221056,C0011633
hasSTY
http://purl.bioontology.org/ontology/STY/T047
mapped from
http://purl.bioontology.org/ontology/MESH/C538250,http://purl.bioontology.org/ontology/MESH/C565166
tui
T047
Instance relations
Types