Terminology Service for NFDI4Health
A sarcoma of the deep layers of the skin. The tumors are locally aggressive tends to recur but rarely metastatic. It can be classified into variants depending on the cell type tumors are derived from or by its characteristics: Pigmented variant from MELANIN-containing DERMAL DENDRITIC CELLS; Myxoid variant, myxoid STROMAL CELLS; Giant cell variant characterized by GIANT CELLS in the tumors; and Fibrosarcomatous variant chracterized by tumor areas histologically indistinguishable from FIBROSARCOMA.
Instance info
Synonyms
Protuberans, Pigmented Dermatofibrosarcoma, Protuberans, Familial Dermatofibrosarcoma, Dermatofibrosarcoma Protuberans, Giant Cell, Fibrosarcomatous Dermatofibrosarcoma Protuberan, DFSPs, Pigmented, Dermatofibrosarcoma Protuberan, Fibrosarcomatous, Darier Ferrand Tumor, Fibrosarcomatous Dermatofibrosarcoma Protuberans, DFSP, Juvenile, Pigmented Dermatofibrosarcoma Protuberans, Familial Dermatofibrosarcoma Protuberan, Dermatofibrosarcoma Protuberan, Dermatofibrosarcoma Protuberans, Myxoid DFSP, Protuberan, Myxoid Dermatofibrosarcoma, Pigmented DFSPs, Dermatofibrosarcoma Protuberans, Metastatic, Myxoid Dermatofibrosarcoma Protuberans, Myxoid DFSPs, Giant Dermatofibrosarcoma Protuberans, Protuberans, Dermatofibrosarcoma, Protuberan, Metastatic Dermatofibrosarcoma, Dermatofibrosarcoma Protuberans, Pigmented, DFSPs, Fibrosarcomatous, Metastatic Dermatofibrosarcoma Protuberans, Protuberans, Metastatic Dermatofibrosarcoma, Dermatofibrosarcoma Protuberans, Myxoid, Bednar Tumor, Metastatic Dermatofibrosarcoma Protuberan, Fibroblastoma, Giant Cell, Dermatofibrosarcoma Protuberan, Myxoid, Juvenile DFSPs, Tumor, Darier-Ferrand, Giant Cell Fibroblastoma, DFSP, Pigmented, Protuberans, Myxoid Dermatofibrosarcoma, Tumor, Bednar's, Dermatofibrosarcoma Protuberans, Giant, Protuberan, Dermatofibrosarcoma, Fibrosarcomatous DFSPs, Cell Fibroblastomas, Giant, Familial Dermatofibrosarcoma Protuberans, Protuberans, Fibrosarcomatous Dermatofibrosarcoma, Protuberan, Familial Dermatofibrosarcoma, Myxoid Dermatofibrosarcoma Protuberan, Fibroblastomas, Giant Cell, Dermatofibrosarkom (DE), Cell Fibroblastoma, Giant, Darier-Ferrand Tumor, Protuberan, Giant Dermatofibrosarcoma, Dermatofibrosarcoma Protuberans, Fibrosarcomatous, Giant Dermatofibrosarcoma Protuberan, Bednars Tumor, Dermatofibrosarcoma Protuberan, Giant, Darier Hoffmann Tumor, Tumor, Bednar, Pigmented DFSP, Protuberans, Giant Dermatofibrosarcoma, Pigmented Dermatofibrosarcoma Protuberan, Dermatofibrosarcoma Protuberan, Metastatic, DFSP, Myxoid, Tumor, Darier-Hoffmann, Dermatofibrosarcoma Protuberans, Familial, Protuberan, Fibrosarcomatous Dermatofibrosarcoma, Fibrosarcomatous DFSP, Juvenile DFSP, Dermatofibrosarcomas, Darier-Hoffmann Tumor, FS-DFSP, Protuberan, Pigmented Dermatofibrosarcoma, DFSP, Fibrosarcomatous, DFSPs, Juvenile, Dermatofibrosarcoma Protuberan, Familial, Bednar's Tumor, Dermatofibrosarcoma Protuberan, Pigmented, Giant Cell Fibroblastomas, DFSPs, Myxoid
AN
/blood supply /chem /second /secret /ultrastruct permitted; coord IM with SKIN NEOPLASMS (IM)
AQL
BL BS CF CH CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SC SU TH UL UR VE VI
DC
1
DX
19940101
HN
94
MDA
19930625
MMR
20140613
MN
C04.557.450.565.590.350.320,C04.557.450.795.350.320
PM
94
QB
http://purl.bioontology.org/ontology/MESH/Q000097,http://purl.bioontology.org/ontology/MESH/Q000175,http://purl.bioontology.org/ontology/MESH/Q000098,http://purl.bioontology.org/ontology/MESH/Q000196,http://purl.bioontology.org/ontology/MESH/Q000151,http://purl.bioontology.org/ontology/MESH/Q000150,http://purl.bioontology.org/ontology/MESH/Q000191,http://purl.bioontology.org/ontology/MESH/Q000139,http://purl.bioontology.org/ontology/MESH/Q000556,http://purl.bioontology.org/ontology/MESH/Q000534,http://purl.bioontology.org/ontology/MESH/Q000378,http://purl.bioontology.org/ontology/MESH/Q000532,http://purl.bioontology.org/ontology/MESH/Q000235,http://purl.bioontology.org/ontology/MESH/Q000652,http://purl.bioontology.org/ontology/MESH/Q000453,http://purl.bioontology.org/ontology/MESH/Q000178,http://purl.bioontology.org/ontology/MESH/Q000134,http://purl.bioontology.org/ontology/MESH/Q000276,http://purl.bioontology.org/ontology/MESH/Q000473,http://purl.bioontology.org/ontology/MESH/Q000000981,http://purl.bioontology.org/ontology/MESH/Q000451,http://purl.bioontology.org/ontology/MESH/Q000737,http://purl.bioontology.org/ontology/MESH/Q000517,http://purl.bioontology.org/ontology/MESH/Q000382,http://purl.bioontology.org/ontology/MESH/Q000469,http://purl.bioontology.org/ontology/MESH/Q000601,http://purl.bioontology.org/ontology/MESH/Q000821,http://purl.bioontology.org/ontology/MESH/Q000523,http://purl.bioontology.org/ontology/MESH/Q000401,http://purl.bioontology.org/ontology/MESH/Q000201,http://purl.bioontology.org/ontology/MESH/Q000266,http://purl.bioontology.org/ontology/MESH/Q000145,http://purl.bioontology.org/ontology/MESH/Q000662,http://purl.bioontology.org/ontology/MESH/Q000188,http://purl.bioontology.org/ontology/MESH/Q000628,http://purl.bioontology.org/ontology/MESH/Q000209,http://purl.bioontology.org/ontology/MESH/Q000648,http://purl.bioontology.org/ontology/MESH/Q000208,http://purl.bioontology.org/ontology/MESH/Q000503
SIB
http://purl.bioontology.org/ontology/MESH/D018319
TERMUI
T841261,T054495,T841260,T853289,T853278,T853277,T853288,T853279,T853274,T853273,T853276,T853275,T853281,T853292,T853280,T853291,T853170,T853294,T853272,T853293,T853290
TH
GHR (2014),ORD (2010),OMIM (2013),NLM (2015),NLM (1994)
cui
C3693482,C0334464,C0334454,C3665732,C0206647
hasSTY
http://purl.bioontology.org/ontology/STY/T191
tui
T191
Instance relations
Types