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Mastocytosis, Systemic

Go to external page http://purl.bioontology.org/ontology/MESH/D034721

A form of systemic mastocytosis in which patients have impaired organ functions due to multifocal infiltrates of pathological MAST CELLS in bone marrow, liver, spleen, gastrointestinal tract, or skeletal system. The cytomorphology shows a low to high grade.

A form of systemic mastocytosis in which patients experience no pain. It is characterized by the multifocal mast cell filtrates, mostly in skin and bone marrow (<20% MAST CELLS). It has a low cytomorphological grade.

A group of disorders caused by the abnormal proliferation of MAST CELLS in a variety of extracutaneous tissues including bone marrow, liver, spleen, lymph nodes, and gastrointestinal tract. Systemic mastocytosis is commonly seen in adults. These diseases are categorized on the basis of clinical features, pathologic findings, and prognosis.

Term info

Label

Mastocytosis, Systemic

Synonyms
  • Aggressive Systemic Mastocytoses
  • Aggressive Systemic Mastocytosis
  • Indolent Systemic Mastocytoses
  • Indolent Systemic Mastocytosis
  • Mast-Cell Disease, Systemic
  • Mast-Cell Diseases, Systemic
  • Mastocytoses, Aggressive Systemic
  • Mastocytoses, Indolent Systemic
  • Mastocytoses, Systemic
  • Mastocytosis, Aggressive Systemic
  • Mastocytosis, Indolent Systemic
  • Mastozytose, systemische (DE)
  • Systemic Mast Cell Disease
  • Systemic Mast-Cell Disease
  • Systemic Mast-Cell Diseases
  • Systemic Mastocytoses
  • Systemic Mastocytoses, Aggressive
  • Systemic Mastocytoses, Indolent
  • Systemic Mastocytosis
  • Systemic Mastocytosis, Aggressive
  • Systemic Mastocytosis, Indolent
  • Systemische Mastozytose (DE)
AQL

BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI

DC

1

DX

20030101

HN

2003

MDA

20020702

MMR

20170620

MN

C20.543.520.350.750, C04.557.450.565.465.750

PM

2003

QB

http://purl.bioontology.org/ontology/MESH/Q000097, http://purl.bioontology.org/ontology/MESH/Q000175, http://purl.bioontology.org/ontology/MESH/Q000196, http://purl.bioontology.org/ontology/MESH/Q000151, http://purl.bioontology.org/ontology/MESH/Q000150, http://purl.bioontology.org/ontology/MESH/Q000191, http://purl.bioontology.org/ontology/MESH/Q000139, http://purl.bioontology.org/ontology/MESH/Q000534, http://purl.bioontology.org/ontology/MESH/Q000235, http://purl.bioontology.org/ontology/MESH/Q000378, http://purl.bioontology.org/ontology/MESH/Q000532, http://purl.bioontology.org/ontology/MESH/Q000652, http://purl.bioontology.org/ontology/MESH/Q000178, http://purl.bioontology.org/ontology/MESH/Q000134, http://purl.bioontology.org/ontology/MESH/Q000453, http://purl.bioontology.org/ontology/MESH/Q000276, http://purl.bioontology.org/ontology/MESH/Q000473, http://purl.bioontology.org/ontology/MESH/Q000000981, http://purl.bioontology.org/ontology/MESH/Q000451, http://purl.bioontology.org/ontology/MESH/Q000517, http://purl.bioontology.org/ontology/MESH/Q000382, http://purl.bioontology.org/ontology/MESH/Q000601, http://purl.bioontology.org/ontology/MESH/Q000821, http://purl.bioontology.org/ontology/MESH/Q000469, http://purl.bioontology.org/ontology/MESH/Q000523, http://purl.bioontology.org/ontology/MESH/Q000401, http://purl.bioontology.org/ontology/MESH/Q000201, http://purl.bioontology.org/ontology/MESH/Q000145, http://purl.bioontology.org/ontology/MESH/Q000266, http://purl.bioontology.org/ontology/MESH/Q000662, http://purl.bioontology.org/ontology/MESH/Q000188, http://purl.bioontology.org/ontology/MESH/Q000628, http://purl.bioontology.org/ontology/MESH/Q000209, http://purl.bioontology.org/ontology/MESH/Q000208, http://purl.bioontology.org/ontology/MESH/Q000503

SIB

http://purl.bioontology.org/ontology/MESH/D034701, http://purl.bioontology.org/ontology/MESH/D034801, http://purl.bioontology.org/ontology/MESH/D012515

TERMUI

T471906, T471905, T471648, T476080

TH

ORD (2010), NLM (2003)

cui

C1112486, C0221013, C0272203

hasSTY

http://purl.bioontology.org/ontology/STY/T191

tui

T191

Term relations

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